An Unusual Presentation of Idiopathic Pulmonary Arterial Hypertension in a Young Male: A Case Report

An Unusual Presentation of Idiopathic Pulmonary Arterial Hypertension in a Young Male: A Case Report

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Idiopathic Pulmonary Arterial Hypertension (IPAH) is a progressive disease of the pulmonary vasculature without any known underlying risk factors.For the diagnosis Pulmonary Artery Hypertension (PAH), the mean Pulmonary Artery Pressure (mPAP) should be bolia outlet gent persistently more than 20 mmHg at rest.Early diagnosis, along with investigations like 2D Echocardiography (ECHO) and right heart catheterisation, and prompt treatment, are essential for the management of PAH.Drugs such as endothelin receptor blockers, phosphodiesterase inhibitors, and calcium channel blockers are used for treatment.Hereby, the authors reported an unusual case of IPAH in a young male, with haemoptysis being the predominant presenting complaint.

A 24-year-old male patient presented with the primary complaints of streaky haemoptysis and dyspnoea.He had multiple hospital admissions for similar episodes of here haemoptysis in the past, which had been managed symptomatically.After conducting a thorough investigation and detailed work-up, he was diagnosed with idiopathic PAH.The patient showed symptomatic improvement, with resolution of haemoptysis and dyspnoea, after initiating treatment.